Tetralogy na Falot

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Tetralogy na Falot
Description (en) Fassara
Iri congenital heart disease (en) Fassara, cyanotic heart defect (en) Fassara, rare genetic developmental defect during embryogenesis (en) Fassara, Ciwon Kwayoyin Halitta, genetic cardiac disease (en) Fassara, Trilogy of Fallot (en) Fassara
cuta
Specialty (en) Fassara cardiac surgery (en) Fassara
pediatrics (en) Fassara
Genetic association (en) Fassara NRP1 (en) Fassara, GPC5 (en) Fassara, JAG1 (en) Fassara, GATA4 (en) Fassara, NKX2-5 (en) Fassara, ZFPM2 (en) Fassara, GATA6 (en) Fassara, GDF1 (en) Fassara da TBX1 (en) Fassara
Suna saboda Arthur Fallot (en) Fassara
Medical treatment (en) Fassara
Magani alprostadil (en) Fassara
Identifier (en) Fassara
ICD-10-CM Q21.3
ICD-9-CM 745.2
OMIM 187500
DiseasesDB 4660
MedlinePlus 001567
eMedicine 001567
MeSH D013771
Disease Ontology ID DOID:6419

Tetralogy na Fallot (TOF) wani nau'in lahani ne na zuciya da ke samuwa a lokacin haihuwa.[1] Alamun a lokacin haihuwa na iya bambanta daga babu zuwa mai tsanani.[2] Daga baya, akwai yawanci lokuta na launin shuɗi zuwa fata da aka sani da cyanosis.[3] Lokacin da jariran da abin ya shafa suka yi kuka ko motsin hanji, za su iya samun “sihiri” inda za su zama shuɗi sosai, suna da wahalar numfashi, su zama rame, wani lokaci kuma su rasa hayyacinsu.[3] Sauran alamomin na iya haɗawa da gunaguni na zuciya, ƙwanƙwasa yatsa, da sauƙin gajiyawa akan shayarwa.[3]

Yawanci ba a san dalilin ba.[4] Abubuwan haɗari sun haɗa da mahaifiyar da ke amfani da barasa, mai ciwon sukari, ta wuce shekaru 40, ko kamuwa da cutar rubella a lokacin daukar ciki.[4][5] Hakanan ana iya haɗa shi da Down syndrome.[4] A al'adance akwai lahani guda huɗu:[1]

  • huhu stenosis, kunkuntar fita daga dama ventricle
  • wani lahani na ventricular septal, rami tsakanin ventricles biyu
  • ventricular hypertrophy na dama, thickening na dama ventricular tsoka
  • Aorta mai wuce gona da iri, wanda ke ba da damar jini daga ventricles biyu don shiga cikin aorta

TOF yawanci ana jinyar ta ta hanyar buɗewar tiyatar zuciya a cikin shekarar farko ta rayuwa.[6] Lokacin tiyata ya dogara da alamun jariri da girmansa.[6] Hanyar ta ƙunshi ƙara girman ƙwayar huhu da jijiyoyi na huhu da gyaran gyare-gyare na ventricular septal.[6] A cikin jariran da suka yi ƙanƙanta, ana iya yin tiyata na wucin gadi tare da tsare-tsare na tiyata na biyu lokacin da jariri ya fi girma.[6] Tare da kulawa mai kyau, yawancin mutanen da abin ya shafa suna rayuwa har su zama manya.[1] Matsalolin na dogon lokaci na iya haɗawa da rashin daidaituwa na bugun zuciya da sakewar huhu.[7]

TOF yana faruwa a kusan 1 cikin 2,000 jarirai.[1] Maza da mata suna shafan daidai.[1] Ita ce mafi yawan hadaddun lahani na cututtukan zuciya wanda ke lissafin kusan kashi 10 na lokuta.[8][9] Niels Stensen ya fara bayyana shi a cikin 1671.[10][11] An buga ƙarin bayanin a cikin 1888 ta likitan Faransa Étienne-Louis Arthur Falot, bayan wanda aka sa masa suna.[10][12] Na farko jimlar gyaran tiyata da aka gudanar a 1954.[7]

Manazarta[gyara sashe | gyara masomin]

  1. 1.0 1.1 1.2 1.3 1.4 "What Is Tetralogy of Fallot?". NHLBI. 1 July 2011. Archived from the original on 4 October 2016. Retrieved 2 October 2016.
  2. Hay, William W.; Levin, Myron J.; Deterding, Robin R.; Abzug, Mark J. (2016-05-02). Current diagnosis & treatment : pediatrics (Twenty-third ed.). New York, NY. ISBN 9780071848541. OCLC 951067614.
  3. 3.0 3.1 3.2 "What Are the Signs and Symptoms of Tetralogy of Fallot?". NHLBI. 1 July 2011. Archived from the original on 5 October 2016. Retrieved 2 October 2016.
  4. 4.0 4.1 4.2 "What Causes Tetralogy of Fallot?". NHLBI. 1 July 2011. Archived from the original on 5 October 2016. Retrieved 2 October 2016.
  5. 6.0 6.1 6.2 6.3 "How Is Tetralogy of Fallot Treated?". NHLBI. July 1, 2011. Archived from the original on 5 October 2016. Retrieved 2 October 2016.
  6. 7.0 7.1 Warnes, Carole A. (July 2005). "The Adult With Congenital Heart Disease". Journal of the American College of Cardiology. 46 (1): 1–8. doi:10.1016/j.jacc.2005.02.083. PMID 15992627.
  7. Yuh, David D. (2014). Johns Hopkins textbook of cardiothoracic surgery (2nd ed.). New York: McGraw-Hill Companies. ISBN 9780071663502. OCLC 828334087.
  8. "Types of Congenital Heart Defects". NHLBI. 1 July 2011. Archived from the original on 5 October 2016. Retrieved 2 October 2016.
  9. 10.0 10.1 "Fallot's tetralogy". Whonamedit?. Archived from the original on 3 October 2016. Retrieved 2 October 2016.
  10. Van Praagh, R (2009). "The first Stella van Praagh memorial lecture: the history and anatomy of tetralogy of Fallot". Seminars in Thoracic and Cardiovascular Surgery. Pediatric Cardiac Surgery Annual. 12: 19–38. doi:10.1053/j.pcsu.2009.01.004. PMID 19349011.
  11. Fallot, Arthur (1888). Contribution à l'anatomie pathologique de la maladie bleue (cyanose cardiaque), par le Dr. A. Fallot, ... (in French). Marseille: Impr. de Barlatier-Feissat. pp. 77–93. OCLC 457786038.CS1 maint: unrecognized language (link)